Es una enfermedad que ocurre en la infancia y niños pequeños (menor a 3 años) que presentan pápulas únicas o múltiples (amarillas, rojas, naranjas o marrones) de 4 a 20 mm en diámetro que puede aparecer en cara, nuca, tronco y en la superficie de las extremidades

Se presenta por igual en niños y niñas y la etiología es desconocida. El diagnostico se realiza mediante biopsia aunque las lesiones son patognomonicas.

El estudio anatomopatologico presenta la presencia de células gigantes de Toutan.

Véase: Xantogranuloma de la región selar

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2: Nakao J, Takano S, Watanabe S, Akutsu H, Matsushita A, Ishii K, Masumoto T, Matsumura A. [Intracerebral xanthogranuloma with specific MRI features: a case report]. No Shinkei Geka. 2011 Nov;39(11):1091-7. Japanese. PubMed PMID: 22036822.

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6: Inoue H, Seichi A, Yamamuro K, Kojima M, Kimura A, Hoshino Y. Dumbbell-type juvenile xanthogranuloma in the cervical spine of an adult. Eur Spine J. 2011 Jul;20 Suppl 2:S343-7. Epub 2011 Apr 6. PubMed PMID: 21468645; PubMed Central PMCID: PMC3111509.

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26: Patil PG, Cummings TJ, Nunley JA, Friedman AH. Xanthogranuloma of the sciatic nerve: case report. Neurosurgery. 2004 Dec;55(6):1435. PubMed PMID: 15574230.

27: Boulos AS, Deshaies EM, Qian J, Popp AJ. Preoperative stent placement for intradural vertebral artery stenosis from a rare xanthogranuloma. Case report. J Neurosurg. 2004 Nov;101(5):864-8. PubMed PMID: 15540929.

28: Takeshima H, Murayama M, Miyanohara O, Nakazato Y, Kuratsu J. Pineal xanthogranuloma. Neurol Med Chir (Tokyo). 2003 Jun;43(6):316-9. PubMed PMID: 12870553.

29: Yonezawa K, Shirataki K, Sakagami Y, Kohmura E. Panhypopituitarism induced by cholesterol granuloma in the sellar region–case report. Neurol Med Chir (Tokyo). 2003 May;43(5):259-62. PubMed PMID: 12790287.

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32: Domínguez J, Castro V, Rivas JJ, Fenández LM, Lorenzo JN, Bravo P. [Symptomatic xanthograuloma of the lateral ventricle]. Neurocirugia (Astur). 2001 Dec;12(6):525-8. Review. Spanish. PubMed PMID: 11787403.

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35: Yamada K, Miura M, Miyayama H, Furuyoshi N, Matsumoto J, Ushio Y. Symptomatic solitary xanthogranuloma occupying the cavernous sinus. Case report. J Neurosurg. 2001 Feb;94(2):322-6. PubMed PMID: 11213973.

36: Mendez-Martinez OE, Luzardo-Small GD, Cardozo-Duran JJ. Symptomatic bilateral xanthogranulomas of choroid plexus in a child. Br J Neurosurg. 2000 Feb;14(1):62-4. PubMed PMID: 10884890.

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39: Tomita H, Tamaki N, Korosue K, Kokunai T. Xanthogranuloma with massive hematoma in the third ventricle: case report. Neurosurgery. 1996 Sep;39(3):591-4. PubMed PMID: 8875492.

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42: Hicks MJ, Albrecht S, Trask T, Byrne ME, Narayan RK, Goodman JC. Symptomatic choroid plexus xanthogranuloma of the lateral ventricle. Case report and brief critical review of xanthogranulomatous lesions of the brain. Clin Neuropathol. 1993 Mar-Apr;12(2):92-6. Review. PubMed PMID: 8386602.

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